Fig. 4
The three indices used for the assessment of ventricular size and the sagittal scout view sequences used for CSF flow quantifications at aqueductal level and C2–C3 level. a a 9-year-old girl with MPS I (Hurler syndrome): Evans’ index (EI) = 0.51. Width of III ventricle (WTV) = 19.4 mm. Callosal angle (CA) = 77.9°. CSF opening pressure (CSF OP) = 17.5 cm H2O. Aqueductal CSF stroke volume (ACSV) = 0.04 ml/CC. Cervical CSF stroke volume (CCSV) = 0 ml/CC; b a 10-year-old boy with MPS II (severe form): EI = 0.42. WTV = 14.9 mm. CA = 52.8°. CSF OP = 40 cm H2O. ACSV = 0.03 ml/CC. CCSV = 0.13 ml/CC; c a 8-year-old boy with MPS III A. EI = 0.43. WTV = 16.8 mm. Callosal angle = 50.7°. CSF opening pressure = 17.5 cm H2O. ACSV = 0.13 ml/CC. CCSV = 0.49 ml/CC